Three cases with papillon-lefevre syndrome
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Derya Uçmak 1 * , Yavuz Yeşilova, Mehmet Nurullah Er, Tuba Dal
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1 Bismil Devlet Hastanesi, Dermatoloji Kliniği, Diyarbakır-Turkey* Corresponding Author

Abstract

Papillon-Lefevre Syndrome is an extremely rare genetic disorder that typically effects infants of approximately one to 5 years of age. Papillon-Lefevre Syndrome is characterized by the development of palmar-plantar hyperkeratosis and early loss of the primary (deciduous) and permanent teeth due to rapidly progressive periodontopathy. The primary (deciduous) teeth frequently become loose and fall out by about five years of age. In the general population, the disorder occurs in approximately one to 4 individuals per 1.000.000. Here we present a Papillon- Lefevre Syndrome case, which is rarely seen, with a review of the literature.

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Article Type: Case Report

J Clin Exp Invest, Volume 2, Issue 2, June 2011, 222-224

https://doi.org/10.5799/ahinjs.01.2011.02.0244

Publication date: 14 Jun 2011

Article Views: 2677

Article Downloads: 2850

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